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FEEDING: MCT-FORMULAS [DD]

FEEDING: MCT-FORMULAS [DD]
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OMIM = Online Mendelian Inheritance of Men

Detail information to gene locus by the National Center for Biotechnology Information NCBI:
less frequent observed after carnitine supplementation in MCT enriched formulas low ratios of
- unsaturated/saturated dicarboxylic acids (<0.1)
- 3-hydroxydecenedioic/3-hydroxydecanedioic acid
- 3-hydroxydodecanedioic/3-hydroxydecanedioic acid (<0.14)
- 3-hydroxyadipic/adipic acid (<0.02) due to MCT ingestion (Tserng 1996)
Laboratory findings    2-Hydroxyadipic acid inc (urine)
    3-Hydroxyadipic acid/Adipic acid inc (urine)
    5-Hydroxyhexanoic acid inc (urine)
    7-Hydroxyoctanoic acid inc (urine)
    Adipic acid inc (urine)
    Dicarboxylic acids inc (urine)
    Sebacic acid inc (urine)
    Suberic acid inc (urine)
Symptoms    no clinical symptoms (probably)
    onset, childhood
    onset, infancy
    onset, neonatal
    Organic acids, urine