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Pyruvic acid
An intermediate compound in the metabolism of carbohydrates, proteins, and fats. In thiamine deficiency, its oxidation is retarded and it accumulates in the tissues, especially in nervous structures. (From Stedman, 26th ed.) Biological Source: Intermediate in primary metabolism including fermentation processes. Present in muscle in redox equilibrium with Lactic acid. A common constituent, as a chiral cyclic acetal linked to saccharide residues, of bacterial polysaccharides. Isolated from cane sugar fermentation broth and peppermint. Constituent of Bauhinia purpurea, Cicer arietinum (chickpea), Delonix regia, Pisum sativum (pea) and Trigonella caerulea (sweet trefoil) Use/Importance: Reagent for regeneration of carbonyl compdounds from semicarbazones, phenylhydrazones and oximes. Flavoring ingredient (Dictionary of Organic Compounds)
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  1. MAPLE SYRUP URINE DISEASE
  2. PROPIONIC ACIDEMIA
  3. ALPHA-MANNOSIDOSIS
  4. PYRUVATE DEHYDROGENASE DEFICIENCY (E3)
  5. PYRUVATE CARBOXYLASE DEFICIENCY
  6. PYRUVATE DEHYDROGENASE DEFICIENCY (E1)
  7. PYRUVATE KINASE DEFICIENCY
  8. MUCOLIPIDOSIS II
  9. TYROSINEMIA III
  10. HYPERPHENYLALANINEMIA DUE TO PTERIN-4a-CARBINOLAMINE DEHYDRATASE
Autoren: Prof. Dr. Friedrich Trefz, Dr. Frauendienst und Hermann Götz. E-Mail: trefz_f@kreiskliniken-reutlingen.de
Last update 29.12.2009 07:05:52