Detail information to gene locus by the National Center for Biotechnology Information NCBI:
  • frequent feeding
  • glucose infusion (acute)
  • high-carbohydrate diet
Ketotic hypoglycaemia is a common form of hypoglycaemia in childhood, should only be diagnosed after exclusion of disorders of carbohydrate or fat metabolism!
ketosis, ketoacidosis
onset, childhood
laboratory finding
Ketone bodies +++urine
Ketone bodies4.0010.00 mmol/lblood
3-Hydroxybutyric acid increased
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