OMIM = Online Medalian Inheritance of Men

Detail information to gene locus by the National Center for Biotechnology Information NCBI:
risk factors probably accounted for hyperammonemia after short bowel resection and/or during PN/TPN:
- short bowel syndrome
- small bowel resection
- excessive intake of branched chain aminoacids
- sufficient quantities of arginine
onset, childhood
onset, infancy
short bowel syndrome (congenital, aquired)
laboratory finding
Ammonia +€mol/lblood
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